- Oral presentation
- Open Access
Spontaneous resolution of a Chiari I malformation and cervicothoracic syrinx in a 9 years old girl with a 47° scoliosis responding favourably to bracing
Scoliosis volume 4, Article number: O58 (2009)
Pediatric case reports support the spontaneous resolution of Chiari I and syrinx. We present a case of a 9 years old girl with a spontaneous regression of a cervico-thoracic syrinx and a complete spontaneous resolution of the Chiari I malformation after one year of bracing to treat her scoliosis.
An 8 years old girl was first diagnosed with JIS. She presented a right thoracic single curve (Apex at T10) of 36° Cobb and ± 10° rotation. Normal sagittal configuration. MRI demonstrated a Chiari I malformation and a cervicothoracic syrinx (C4 to T9-10). She attended our clinic later showing a rapid progression of the Cobb angle to 47° Cobb. Absent superficial abdominal reflexes was the only neurological sign. Bracing with a RSC was indicated. After one year of treatment (in brace correction 47%) the scoliometer value reduced from a total value of 9.5° to 6°. Back asymmetry has dramatically improved. A second MRI showed a reduced syrinx and no Chiari I malformation.
Discussion and conclusion
This is a first report of a case showing a temporary improvement of a conservatively treated scoliosis coinciding with a spontaneous resolution of a Chiari I malformation and a related cervico-thoracic syrinx. The mechanism of such a resolution is not clear. However this case supports the idea that the resolution of the Chiari I and its related syrinx would improve the prognosis of the associated scoliosis.
Morcuende JA, Dolan LA, Vazquez JD, Jirasirakul A, Weinstein SL: A prognosis model for the presence of neurogenic lesions in atypical idiopathic scoliosis. Spine. 2004, 29 (1): 51-8. 10.1097/01.BRS.0000105526.65485.92.
Sun PP, Harrop J, Sutton LN, Younkin D: Complete spontaneous resolution of childhood Chiari I malformation and associated syringomyelia. Pediatrics. 2001, 107 (1): 182-4. 10.1542/peds.107.1.182.
Kyoshima K, Bogdanov EI: Spontaneous resolution of syringomyelia: report of two cases and review of the literature. Neurosurgery. 2003, 53 (3): 762-8. 10.1227/01.NEU.0000079629.05048.A2. discussion 768–9.
Guillem A, Costa JM: Spontaneous resolution of Chiari I malformation associated syringomyelia in one child. Acta Neurochir (Wien). 2004, 146 (2): 187-91. 10.1007/s00701-003-0177-0.
Coppa ND, Kim HJ, McGrail KM: Spontaneous resolution of syringomyelia and Chiari malformation type I in a patient with cerebrospinal fluid otorrhea. Case report. J Neurosurg. 2006, 105 (5): 769-71. 10.3171/jns.2006.105.5.769.
About this article
Cite this article
Rigo, M., Martinez, L.M.G. Spontaneous resolution of a Chiari I malformation and cervicothoracic syrinx in a 9 years old girl with a 47° scoliosis responding favourably to bracing. Scoliosis 4, O58 (2009). https://doi.org/10.1186/1748-7161-4-S1-O58
- Public Health
- Rapid Progression
- Cobb Angle
- Neurological Sign
- Pediatric Case